dentin dysplasia type i with hypomature amelogenesis imperfecta in an 18-year-old girl

نویسندگان

ehsan azma department of oral medicine, guilan university of medical sciences, dental school, rasht, iran

seyed javad kia department of oral medicine, guilan university of medical sciences, dental school, rasht, iran

somayeh nemati department of maxillofacial radiology, guilan university of medical sciences, dental faculty, rasht, iran

چکیده

introduction: dentin dysplasia is a rare autosomal dominant inheriting disturbance of dentin formation characterized by normal enamel formation, but atypical dentin with abnormal pulpal morphology. there are two major patterns: type i and type ii. amelogenesis imperfecta is an autosomal dominant. x-link inherent disease that is classified by clinical manifestation into hypoplastic, hypomature, hypocalcified. the simultaneous occurrence of dentin dysplasia and amelogenesis imperfecta is quite rare. the purpose of this case report is to pre-sent a case of dentin dysplasia type i which is also associated with hypoplastic amelogenesis imperfecta in an 18 year old girl, without any syndromic signs.

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عنوان ژورنال:
journal of dentomaxillofacil radiology, pathology and surgery

جلد ۲، شماره ۳، صفحات ۳۴-۳۹

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